Referring Patients for PAH-CTD Diagnosis

Co-management of Patients With PAH-CTD

Rheumatologists are integral to the detection and co-management of PAH associated with systemic sclerosis (PAH-SSc). The identification, diagnosis, and management of PAH-SSc requires collaboration among pulmonologists, cardiologists, and rheumatologists.1,2 Given the complex nature of PAH and its diagnosis and management, it is important to consider partnering with specialists who have experience in managing this condition.2-4

PARTNERSHIP of PAH-SSc specialists
PAH-CTD medical spcialists flow chart
African American patients with PAH-SSc may be diagnosed with more severe disease.5 Find Out How They May Be at Greater Risk >


Utilizing the Pulmonary Hypertension Association’s network of Centers of Comprehensive Care and Regional Clinical Programs to collaborate with appropriate specialists may reduce PAH-SSc diagnosis delay and improve outcomes.6

PAH-CTD=pulmonary arterial hypertension associated with connective tissue disease.
References: 1. Minai OA, Budev MM. Diagnostic strategies for suspected pulmonary arterial hypertension: a primer for the internist. Cleve Clin J Med. 2007;74(10):737-747. 2. McLaughlin VV, Shah SJ, Souza R, Humbert M. Management of pulmonary arterial hypertension. J Am Coll Cardiol. 2015;65(18):1976-1997. 3. Strange G, Fowler R, Jary C, Dalton B, Stewart S, Gabbay E. Integrated care and optimal management of pulmonary arterial hypertension. J Multidiscip Healthc. 2009;2:67-78. 4. Deaño RC, Glassner-Kolmin C, Rubenfire M, et al. Referral of patients with pulmonary hypertension diagnoses to tertiary pulmonary hypertension centers: the multicenter RePHerral study. JAMA Intern Med. 2013;173(10):887-893. 5. Blanco I, Mathai S, Shafiq M, et al. Severity of systemic sclerosis-associated pulmonary arterial hypertension in African Americans. Medicine (Baltimore). 2014;93(5):177-185. 6. Mandras SA, Ventura HO, Corris PA. Breaking down the barriers: why the delay in referral for pulmonary arterial hypertension? Ochsner J. 2016;16(3):257-262.